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(Circulation. 1967;35:783.)
© 1967 American Heart Association, Inc.

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Gaucher's Disease of the Lung Causing Severe Pulmonary Hypertension with Associated Acute Recurrent Pericarditis

WILLIAM C. ROBERTS M.D.¹ DONALD S. FREDRICKSON M.D.¹

¹ From the Laboratory of Pathology, Clinic of Surgery and Laboratory of Molecular Diseases, National Heart Institute, National Institutes of Health, Bethesda, Maryland.

The clinical and pathological features of a 30-year-old man with Gaucher's disease are described. He had severe pulmonary hypertension resulting from obstruction of pulmonary capillaries by Gaucher cells. Acute recurrent pericarditis of unknown etiology terminally led to hemopericardium and cardiac tamponade.

Key Words: Cerebral involvement • Elastic fibers • Bronchial constriction • Cor pulmonale • Anemia • Ruptured pericardial vessels

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