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(Circulation. 1969;40:377.)
© 1969 American Heart Association, Inc.

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Progressive Muscular Dystrophy

Hemodynamic, Angiographic, and Pathologic Study of a Patient with Myocardial Involvement

MARTIAL A. DEMANY M.D.¹ HENRY A. ZIMMERMAN M.D.¹

¹ From the Marie L. Coakley Cardiovascular Laboratory, Saint Vincent Charity Hospital, Cleveland, Ohio.

This paper describes the case of a young man with progressive muscular dystrophy who had supraventricular arrhythmias and intractable congestive failure. Hemodynamic studies and left cineventriculographic findings were compatible with a diagnosis of severe left ventricular failure.

Coronary cinearteriography showed an abrupt ending of the artery to the sino-atrial node. At necropsy, a noninflammatory degeneration was found in this particular vessel. The pathogenesis of the cardiac arrhythmias seen in this condition is discussed in the light of these cineangiographic and histopathologic observations.

Key Words: Supraventricular arrhythmia • Cinecoronary arteriograms • Congestive heart failure • Necropsy study