This Article Full Text (PDF) Alert me when this article is cited Alert me if a correction is posted Services Email this article to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal Download to citation manager Request Permissions Citing Articles Citing Articles via HighWire Citing Articles via Google Scholar Google Scholar Articles by GOMES, M. M. R. Articles by DANIELSON, G. K. Search for Related Content PubMed PubMed Citation Articles by GOMES, M. M. R. Articles by DANIELSON, G. K.

(Circulation. 1971;43:889.)
© 1971 American Heart Association, Inc.

---

Double-Outlet Right Ventricle with Pulmonic Stenosis

Surgical Considerations and Results of Operation

MANUEL M. R. GOMES M.D.¹; WILLIAM H. WEIDMAN M.D.¹; DWIGHT C. MCGOON M.D.¹; GORDON K. DANIELSON M.D.¹

¹ From the Mayo Graduate School of Medicine and the Mayo Clinic and Mayo Foundation, Rochester, Minnesota 55901.

The results of complete repair of double-outlet right ventricle with pulmonic stenosis in 22 Mayo Clinic patients were analyzed. The overall mortality rate was 32%. Since 1960, the mortality rate has been reduced to 16%. Anomalies of the distribution of the right coronary artery, a second ventricular septal defect of the atrioventricular canal type, and significant residual pulmonic stenosis were associated with a higher mortality rate. The difficulties in the diagnosis of this uncommon condition are emphasized.

Complete repair is best carried out after the patient is 4 years old. A systemic-to-pulmonary arterial shunt is the procedure of choice for those who are younger than this. In the occasional patient with anomalous distribution of the right coronary artery which precludes adequate relief of the pulmonic stenosis, use of an aortic homograft from the right ventricle to the pulmonary artery should be considered.

Key Words: Ventricular septal defect • Cardiac surgery • Cardiac anomalies

Submitted on October 5, 1970
Accepted on February 22, 1971

This article has been cited by other articles:

				A. Skoulas, R. Franklin, and R. Cardelli Double-Outlet Right Ventricle With Long Survival Angiology, September 1, 1977; 28(9): 619 - 623. [Abstract] [PDF]