Circulation, Vol 53, 157-161, Copyright © 1976 by American Heart Association
BA Vidne, S Subramanian and HR Wagner
In patients with transposition of the great arteries (TGA), both the D- and
L- forms, an aneurysm of the membranous ventricular septum (AMS) produces
subpulmonic stenosis due to the higher right ventricular pressure which
forces the aneurysm to protrude into the left ventricular, i.e.,
subpulmonic, outflow tract. The clinical signs and symptoms, hemodynamic
findings as well as surgical results were analyzed in eight patients with
TGA and AMS. The presence of an AMS should be suspected from hemodynamic
data consisting of a combination of elevated left ventricular pressure,
gradient across the left ventricular outflow tract and presence of a small
ventricular septal defect with or without pulmonary artery hypertension.
The AMS can be demonstrated by a right ventricular injection in the lateral
view. The anomaly needs to be corrected at the time of the Mustard
procedure. If uncorrected it may lead to postoperative death or progressive
obstruction. In the presence of an aneurysm even small ventricular septal
defects should be closed by a patch and the aneurysm should be excised.
ARTICLES
Aneurysm of the membranous ventricular septum in transposition of the great arteries
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