Circulation, Vol 66, 266-272, Copyright © 1982 by American Heart Association
C Bull, MR de Leval, C Mercanti, FJ Macartney and RH Anderson
The dismal outlook for patients with pulmonary atresia with intact
ventricular septum may be related to associated right ventricular
hypoplasia. Study of 32 autopsy specimens and 46 angiocardiograms of
neonates with this lesion suggested that the cavitary hypoplasia was
related to massive hypertrophy of the right ventricular wall. This
hypertrophy was sufficient to obliterate the trabecular and/or infundibular
portion of the ventricular cavity entirely in one-third of the cases; this
observation forms the basis for a revised classification of these hearts.
Three autopsies and 14 angiograms of neonates with critical pulmonary
stenosis were examined. Hearts with obliterated infundibular and trabecular
cavities had thicker walls and smaller tricuspid valves, as estimated
angiographically or at autopsy, than those in which the normal three
portions of the ventricular cavity were represented.
ARTICLES
Pulmonary atresia and intact ventricular septum: a revised classification
This article has been cited by other articles:
 |
|
 |
|
  Y. Hirata, J. M. Chen, J. M. Quaegebeur, W. E. Hellenbrand, and R. S. Mosca Pulmonary Atresia With Intact Ventricular Septum: Limitations of Catheter-Based Intervention Ann. Thorac. Surg., August 1, 2007; 84(2): 574 - 580. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
K. J. Guleserian, L. B. Armsby, R. R. Thiagarajan, P. J. del Nido, and J. E. Mayer Jr Natural History of Pulmonary Atresia With Intact Ventricular Septum and Right-Ventricle-Dependent Coronary Circulation Managed by the Single-Ventricle Approach Ann. Thorac. Surg., June 1, 2006; 81(6): 2250 - 2258. [Abstract] [Full Text] [PDF]
|
|
|
|
 |
|
 J. Odim, H. Laks, and T. Tung Risk factors for early death and reoperation following biventricular repair of pulmonary atresia with intact ventricular septum. Eur. J. Cardiothorac. Surg., May 1, 2006; 29(5): 659 - 665. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
J. Odim, H. Laks, M. D. Plunkett, and T. C. Tung Successful Management of Patients With Pulmonary Atresia With Intact Ventricular Septum Using a Three Tier Grading System for Right Ventricular Hypoplasia Ann. Thorac. Surg., February 1, 2006; 81(2): 678 - 684. [Abstract] [Full Text] [PDF]
|
|
|
|
 |
|
 K. Miyaji, A. Murakami, T.-i. Takasaki, K. Ohara, S. Takamoto, and H. Yoshimura Does a bidirectional Glenn shunt improve the oxygenation of right ventricle-dependent coronary circulation in pulmonary atresia with intact ventricular septum? J. Thorac. Cardiovasc. Surg., October 1, 2005; 130(4): 1050 - 1053. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
P. E.F. Daubeney, D. Wang, D.J. Delany, B.R. Keeton, R.H. Anderson, Z. Slavik, M. Flather, S.A. Webber, and for the UK and Ireland Collaborative Study of Pulm Pulmonary atresia with intact ventricular septum: Predictors of early and medium-term outcome in a population-based study J. Thorac. Cardiovasc. Surg., October 1, 2005; 130(4): 1071 - 1071. [Abstract] [Full Text] [PDF]
|
|
|
|
 |
|
 Y P Mi, A K T Chau, C S W Chiu, T C Yung, K S Lun, and Y F Cheung Evolution of the management approach for pulmonary atresia with intact ventricular septum Heart, May 1, 2005; 91(5): 657 - 663. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
N. Yoshimura, M. Yamaguchi, H. Ohashi, Y. Oshima, S. Oka, M. Yoshida, H. Murakami, and T. Tei Pulmonary atresia with intact ventricular septum: Strategy based on right ventricular morphology J. Thorac. Cardiovasc. Surg., November 1, 2003; 126(5): 1417 - 1426. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
A. Ansari, D. Goltz, K. P. McCarthy, A. Cook, and S. Y. Ho The conduction system in hearts with pulmonary atresia and intact ventricular septum Ann. Thorac. Surg., May 1, 2003; 75(5): 1502 - 1505. [Abstract] [Full Text] [PDF]
|
|
|
|
 |
|
 P. E. F. Daubeney, D. J. Delany, R. H. Anderson, G. G. S. Sandor, Z. Slavik, B. R. Keeton, S. A. Webber, and for the United Kingdom and Ireland Collaborative S Pulmonary atresia with intact ventricular septum: Range of morphology in a population-based study J. Am. Coll. Cardiol., May 15, 2002; 39(10): 1670 - 1679. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
S. Sano, K. Ishino, M. Kawada, E. Fujisawa, M. Kamada, and S.-i. Ohtsuki Staged biventricular repair of pulmonary atresia or stenosis with intact ventricular septum Ann. Thorac. Surg., November 1, 2000; 70(5): 1501 - 1506. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
J. Rychik, H. Levy, J. W. Gaynor, W. M. DeCampli, and T. L. Spray OUTCOME AFTER OPERATIONS FOR PULMONARY ATRESIA WITH INTACT VENTRICULAR SEPTUM J. Thorac. Cardiovasc. Surg., December 1, 1998; 116(6): 924 - 931. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
C. Ovaert, S. A. Qureshi, E. Rosenthal, E. J. Baker, and M. Tynan Growth of the right ventricle after successful transcatheterpulmonary valvotomy in neonates and infants with pulmonary atresia and intactventricular septum J. Thorac. Cardiovasc. Surg., May 1, 1998; 115(5): 1055 - 1059. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
K. Miyaji, M. Shimada, A. Sekiguchi, A. Ishizawa, T. Isoda, and M. Tsunemoto Pulmonary Atresia With Intact Ventricular Septum: Long-Term Results of ``One and a Half Ventricular Repair'' Ann. Thorac. Surg., December 1, 1995; 60(6): 1762 - 1764. [Abstract] [Full Text]
|
|
|
|
|
|
J. D. Waldman, R. B. Karp, J. J. Lamberti, M. E. Sand, D. G. Ruschhaupt, and B. Agarwala Tricuspid Valve Closure in Pulmonary Atresia and Important RV-to-Coronary Artery Connections Ann. Thorac. Surg., April 1, 1995; 59(4): 933 - 940. [Abstract] [Full Text]
|
|
|
|
|
|
C. Bull, M. Kostelka, K. Sorensen, and M. de Leval Outcome measures for the neonatal management of pulmonary atresia with intact ventricular septum J. Thorac. Cardiovasc. Surg., February 1, 1994; 107(2): 359 - 366. [Abstract] [Full Text]
|
|