Circulation. 2000;102:e14-e15
(Circulation. 2000;102:e14.)
© 2000 American Heart Association, Inc.
Circulation Electronic Pages |
Right Ventricular Myxoma Obstructing the Right Ventricular Outflow Tract
Jeffrey H. Kern, MD;
Flor A. Aguilera, MD;
Diane L. Carlson, MD;
Mark Galantowicz, MD
From The New York Presbyterian Hospital, Departments of Pediatrics,
Pathology, and Surgery, New York, NY.
Correspondence to Jeffrey H. Kern, MD, Division of Pediatric Cardiology, The New York Hospital–Cornell Medical Center, 525 E 68th St, New York, NY 10021. E-mail jhkern{at}mail.med.cornell.edu
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Introduction
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 Top
 Introduction
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A12-year-old
previously healthy girl developed syncope when
walking at school. When
she was seen in the emergency department,
her heart rate was 115 bpm,
the precordial impulse was active,
and a thrill was palpated. Third
and fourth heart sounds were
heard. A grade 4/6 systolic
ejection murmur was heard at the
left upper sternal border. The chest
x-ray demonstrated a mildly
enlarged, globular heart. Diffuse T-wave
changes were seen on
the ECG.
Echocardiography revealed a cardiac mass
extending
from the right ventricle across the pulmonic valve into the
pulmonary
artery (Figure 1
). The
mass was removed under cardiopulmonary
bypass. The tumor
measured 7
x4
x2 cm and was found to be a myxoma
(Figures 2
and 3
).
Postoperative echocardiography documented
an
unobstructed right ventricular outflow tract (Figure 4
).
Myxomas, particularly those located
in the right ventricular
outflow tract, are exceedingly
rare in pediatric patients.
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Figure 1. Echocardiogram demonstrating tumor crossing right
ventricular outflow tract. RV indicates right ventricle; T,
tumor; and PA, pulmonary artery.
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Footnotes
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The editor of Images in Cardiovascular Medicine is Hugh A. McAllister,
Jr, MD, Chief, Department of Pathology, St Luke’s Episcopal
Hospital and Texas Heart Institute, and Clinical Professor of
Pathology, University of Texas Medical School and Baylor College
of Medicine.
Circulation encourages readers to submit cardiovascular images to the Circulation Editorial Office, St Luke’s Episcopal Hospital/Texas Heart Institute, 6720 Bertner Ave, MC1-267, Houston, TX 77030.
